Presentation
More than 90% of cases present in the first year of life with up to 25% being congenital 1. There is a reported male:female ratio of 2:1 but the exact incidence is unknown 2. [radiopaedia.org]
In this report, we describe eight additional patients and present a compilation of the clinical statistics of all 75 cases. (Arch Dermatol 1989;125:88-91) [jamanetwork.com]
Most cases presented as solitary masses, but four cases of multiple separate synchronous lesions have been reported. Most lesions presented as a painless nodule, sometimes with rapid growth. [journals.sagepub.com]
Entire Body System
- Fishing
Fluorescent in situ hybridization (FISH) was neg Lenguage dc.language.iso en Publisher dc.publisher Sociedad Chilena de Pediatria Type of license dc.rights Attribution-NonCommercial-NoDerivs 3.0 Chile Link to License dc.rights.uri http://creativecommons.org [repositorio.uchile.cl]
Skin
- Subcutaneous Mass
mass with intersecting bands of fibrous signal tissue in the appropriate age group is highly suggestive of the diagnosis. [radiopaedia.org]
Treatment
COMMENTS: We describe the case, its differential diagnosis and the immunhistological characteristics, and we discuss the non-aggressive surgical treatment, based on the benign behaviour of this tumour. [ncbi.nlm.nih.gov]
Treatment and prognosis Local excision is usually curative since recurrence is uncommon. [radiopaedia.org]
However, in order to reach a precise diagnosis and plan treatment, clinical heterogeneity obliges us to become familiar with variations in the characteristic triphasic histology of FHI. [repositorio.uam.es]
The treatment of choice is local excision. Even with incomplete excision, FHI has a low recurrence rate. [journals.sagepub.com]
Prognosis
Treatment and prognosis Local excision is usually curative since recurrence is uncommon. [radiopaedia.org]
Epidemiology
Definition / general Tumor-like condition in newborns to 2 year olds Poorly circumscribed proliferation of immature spindle cells in organoid pattern with fat and dense fibrocollagenous tissue Epidemiology Rare; usually age 2 years or less (25% discovered [pathologyoutlines.com]